Pascale Bomont – PGNM

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Elisabeth Cortier

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Projects

Neurofilaments in health and neurodegenerative disease

In this project, we combine state-of-the-art live-imaging, proteomics and mathematic modelization to study the dynamics of neurofilaments in vivo, using […]

Dynamics of autophagy within neurons

The project combines cell biology, live-imaging and biophysics, to study the spatial control of autophagy within neuron, and subsequent alterations […]

Therapy for Giant Axonal Neuropathy

In this project, we will use the robust animal models (mouse & zebrafish) we generated for GAN. The goal is […]

Publications

Liénard C, Pradeilles N, Cortier E, Hassen-Khodja C, Arias L, Ceprian-Costoso M, Picot A, Mausset-B..., Disease mutation in gigaxonin-E3 ligase recapitulates giant axonal neuropathy in mice., Acta Neuropathol Commun 2025 Dec; 14(1): 20.

van Asperen JV, Kotaich F, Caillol D, Bomont P, Neurofilaments: Novel findings and future challenges., Curr Opin Cell Biol 2024 Apr; 87(): 102326.

Liénard C, Pintart A, Bomont P, Neuronal Autophagy: Regulations and Implications in Health and Disease., Cells 2024 Jan; 13(1): .

Lescouzères L, Hassen-Khodja C, Baudot A, Bordignon B, Bomont P, A multilevel screening pipeline in zebrafish identifies therapeutic drugs for GAN., EMBO Mol Med 2023 Jul; 15(7): e16267.

Lescouzères L, Bordignon B, Bomont P, Development of a high-throughput tailored imaging method in zebrafish to understand and treat neuromuscular diseases., Front Mol Neurosci 2022 ; 15(): 956582.